Brief Report: Repetitive Behaviour Profiles in Williams syndrome: Cross Syndrome Comparisons with Prader–Willi and Down syndromes
Royston, Rachel Oliver, Chris Moss, Joanna Adams, Dawn Berg, Katy Burbidge, Cheryl Howlin, Patricia Nelson, L Stinton, Christopher Waite, Jane
Royston, Rachel
Oliver, Chris
Moss, Joanna
Adams, Dawn
Berg, Katy
Burbidge, Cheryl
Howlin, Patricia
Nelson, L
Stinton, Christopher
Waite, Jane
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Affiliation
University of Birmingham; Griffith University; University of East London; Coventry and Warwickshire Partnership NHS Trust; King’s College London; University of Sydney; University of Warwick
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Publication date
2017-10-04
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Abstract
This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader–Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader–Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.
Citation
Royston, R., Oliver, C., Moss, J. et al. Brief Report: Repetitive Behaviour Profiles in Williams syndrome: Cross Syndrome Comparisons with Prader–Willi and Down syndromes. J Autism Dev Disord 48, 326–331 (2018). https://doi.org/10.1007/s10803-017-3319-6
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Article